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It certainly fills up spaces in the great jigsaw puzzle...
Nic 63/21
On 11 November 2015 at 04:00, Kathleen Cochran <[log in to unmask]> wrote:
> Very interesting. Does this relate somehow to inosine, which affects urate
> levels? And might this have something to do with how dogs pick up the smell
> of PD?
>
> I swear, for the last year or so, I've been aware of an ammonia smelll that
> seems to emanate from me. I wonder if this smell masks other odors,
> resulting in the anosmia experienced by many of us PD sufferers.
>
> Could PD be a urea cycle disorder?
>
> Kathleen
>
>
>
> -----------------------------------------------------------------------------------------------------------------------------------------------------
>
> From the University of Rochester, here is something on ammonia testing.
>
> Link:
>
>
> https://www.urmc.rochester.edu/encyclopedia/content.aspx?ContentTypeID=167&ContentID=ammonia
> Ammonia Does this test have other names?
>
> Blood ammonia test, NH3
> What is this test?
>
> This test checks the level of ammonia in your blood. The test helps find
> out why you may have changes in consciousness and also helps diagnose a
> liver disease called hepatic encephalopathy. This disease affects how your
> brain works, because of excess toxins, or poisons, in your body.
>
> Your liver may not work properly if you have high levels of ammonia in your
> blood. Ammonia is a chemical made by bacteria in your intestines and your
> body's cells while you process protein. Your body treats ammonia as a waste
> product. It turns it into an amino acid called glutamine and a chemical
> compound called urea. Your bloodstream moves the urea to your kidneys,
> where it is eliminated in your urine.
>
> But ammonia will build up in your body if you can't get rid of urea. This
> can sometimes happen if you have kidney or liver failure. It can also
> happen if you have a urea cycle disorder, a genetic disorder that means
> your body is missing one of the enzymes that remove ammonia from the blood.
> The ammonia blood test is the gold standard for diagnosing urea cycle
> disorders.
>
> On 9 November 2015 at 20:04, Rayilyn Brown <[log in to unmask]> wrote:
>
> > another abstract from Joanie McGuire
> >
> > Program#/Poster#:
> > 12.02
> >
> >
> >
> >
> > Presentation Title:
> > Stopping progression of Parkinson's disease with the drug
> > phenylbutyrate
> >
> >
> >
> >
> > Location:
> > N230
> >
> >
> >
> >
> > Presentation time:
> > Saturday, Oct 17, 2015, 1:15 PM - 1:30 PM
> >
> >
> >
> >
> > Topic:
> > ++C.03.a. Human studies
> >
> >
> >
> >
> > Authors:
> > *C. R. FREED1, M. WANG1, J. CUMMISKEY1, K. B. BJUGSTAD1, B. A.
> > SYMMES1, C. A. JOHNSON2, R. C. MURPHY2, M. A. LEEHEY3, W. ZHOU1;
> > 1Div. of Clin. Pharmacol., 2Dept. of Pharmacol., 3Dept. of
> > Neurol., Univ. Colorado Sch. of Med., Aurora, CO
> >
> >
> >
> >
> > Abstract:
> > Parkinson's disease has excellent symptomatic treatment with
> > drugs such as L-DOPA, but the underlying disease process causes a
> > relentless downhill course.
> >
> >
> >
> > Several drugs have been tested in an effort to alter disease
> > progression, but all have failed. We have developed a new concept for
> > stopping the progression of Parkinson’s disease by turning on a
> > neuroprotective gene with an FDA-approved drug. In Parkinson’s disease,
> the
> > protein alpha-synuclein forms abnormal deposits called Lewy bodies as
> well
> > as toxic fibrils which contribute to the death of dopamine neurons. We
> have
> > discovered that the drug phenylbutyrate can prevent aggregation of
> > alpha-synuclein in transgenic mice which are genetically programmed to
> > develop a form of Parkinson’s disease as they age.
> >
> >
> >
> > The drug works by upregulating the neuroprotective gene DJ-1.
> > Gene activation leads to an increase in lysosome and exosome activity,
> > promoting transfer of alpha-synuclein from neurons into the bloodstream
> > where the protein is eliminated. In mice, phenylbutyrate increased plasma
> > alpha-synuclein by about 100 per cent compared to non-treated control
> > animals.
> >
> >
> >
> > To see if phenylbutyrate has the same effect in people, we
> > have given the drug for three weeks to 20 people with newly diagnosed
> > Parkinson’s disease and to 20 age-matched subjects without the disease.
> We
> > found that the drug increased the level of alpha-synclein in plasma of
> all
> > 40 subjects from 50 to 150 per cent of baseline values, just as it had
> done
> > in transgenic mice, strongly suggesting that the drug can mobilize
> > alpha-synuclein from neurons into blood plasma. While baseline plasma
> > alpha-synuclein varied between subjects, the average alpha-synuclein
> plasma
> > concentrations at baseline and during phenylbutyrate administration did
> not
> > differ between patients with Parkinson's disease and normal subjects.
> > Results are compatible with a neuroprotective effect of phenylbutyrate by
> > accelerating clearance of alpha-synuclein from brain into plasma.
> >
> >
> >
> > A double-blind, placebo-controlled trial in newly diagnosed
> > Parkinson patients will be needed to prove whether phenylbutyrate can
> stop
> > the progression of Parkinson’s disease in humans.
> >
> >
> >
> >
> > Disclosures:
> > C.R. Freed: C. Other Research Support (receipt of drugs,
> > supplies, equipment or other in-kind support); Hyperion Pharmaceuticals.
> M.
> > Wang: None. J. Cummiskey: None. K.B. Bjugstad: None. B.A. Symmes:None.
> C.A.
> > Johnson: None. R.C. Murphy: None. M.A. Leehey: None. W. Zhou: None.
> >
> >
> >
> >
> > Keyword (s):
> > PARKINSON'S DISEASE
> >
> >
> >
> >
> >
> > NEUROPROTECTION
> >
> >
> >
> >
> >
> > DOPAMINE
> >
> >
> >
> >
> > Support:
> > Walter S. and Lucienne Driskill Foundation
> >
> >
> >
> >
> >
> > Michael J. Fox Foundation
> >
> >
> >
> >
> >
> > Mr. Charles Ackerman
> >
> >
> >
> >
> >
> > Mr. Ray Sidhom
> >
> >
> >
> >
> >
> > Mr. John Anderson
> >
> >
> >
> >
> >
> >
> >
> >
> > Ray
> > Rayilyn Brown
> > Past Director AZNPF
> > Arizona Chapter National Parkinson Foundation
> >
> > ----------------------------------------------------------------------
> > To sign-off Parkinsn send a message to: mailto:
> > [log in to unmask]
> > In the body of the message put: signoff parkinsn
> >
>
> ----------------------------------------------------------------------
> To sign-off Parkinsn send a message to: mailto:
> [log in to unmask]
> In the body of the message put: signoff parkinsn
>
----------------------------------------------------------------------
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2 February 2001, Week 1 January 2001, Week 5 January 2001, Week 4 January 2001, Week 3 January 2001, Week 2 January 2001, Week 1 December 2000, Week 5 December 2000, Week 4 December 2000, Week 3 December 2000, Week 2 December 2000, Week 1 November 2000, Week 5 November 2000, Week 4 November 2000, Week 3 November 2000, Week 2 November 2000, Week 1 October 2000, Week 5 October 2000, Week 4 October 2000, Week 3 October 2000, Week 2 October 2000, Week 1 September 2000, Week 5 September 2000, Week 4 September 2000, Week 3 September 2000, Week 2 September 2000, Week 1 August 2000, Week 5 August 2000, Week 4 August 2000, Week 3 August 2000, Week 2 August 2000, Week 1 July 2000, Week 5 July 2000, Week 4 July 2000, Week 3 July 2000, Week 2 July 2000, Week 1 June 2000, Week 5 June 2000, Week 4 June 2000, Week 3 June 2000, Week 2 June 2000, Week 1 May 2000, Week 5 May 2000, Week 4 May 2000, Week 3 May 2000, Week 2 May 2000, Week 1 April 2000, Week 5 April 2000, Week 4 April 2000, Week 3 April 2000, Week 2 April 2000, Week 1 March 2000, Week 5 March 2000, Week 4 March 2000, Week 3 March 2000, Week 2 March 2000, Week 1 February 2000, Week 5 February 2000, Week 4 February 2000, Week 3 February 2000, Week 2 February 2000, Week 1 January 2000, Week 5 January 2000, Week 4 January 2000, Week 3 January 2000, Week 2 January 2000, Week 1 December 1999, Week 5 December 1999, Week 4 December 1999, Week 3 December 1999, Week 2 December 1999, Week 1 November 1999, Week 5 November 1999, Week 4 November 1999, Week 3 November 1999, Week 2 November 1999, Week 1 October 1999, Week 5 October 1999, Week 4 October 1999, Week 3 October 1999, Week 2 October 1999, Week 1 September 1999, Week 5 September 1999, Week 4 September 1999, Week 3 September 1999, Week 2 September 1999, Week 1 August 1999, Week 5 August 1999, Week 4 August 1999, Week 3 August 1999, Week 2 August 1999, Week 1 July 1999, Week 5 July 1999, Week 4 July 1999, Week 3 July 1999, Week 2 July 1999, Week 1 June 1999, Week 5 June 1999, Week 4 June 1999, Week 3 June 1999, Week 2 June 1999, Week 1 May 1999, Week 5 May 1999, Week 4 May 1999, Week 3 May 1999, Week 2 May 1999, Week 1 April 1999, Week 5 April 1999, Week 4 April 1999, Week 3 April 1999, Week 2 April 1999, Week 1 March 1999, Week 5 March 1999, Week 4 March 1999, Week 3 March 1999, Week 2 March 1999, Week 1 February 1999, Week 4 February 1999, Week 3 February 1999, Week 2 February 1999, Week 1 January 1999, Week 5 January 1999, Week 4 January 1999, Week 3 January 1999, Week 2 January 1999, Week 1 December 1998, Week 5 December 1998, Week 4 December 1998, Week 3 December 1998, Week 2 December 1998, Week 1 November 1998, Week 5 November 1998, Week 4 November 1998, Week 3 November 1998, Week 2 November 1998, Week 1 October 1998, Week 5 October 1998, Week 4 October 1998, Week 3 October 1998, Week 2 October 1998, Week 1 September 1998, Week 5 September 1998, Week 4 September 1998, Week 3 September 1998, Week 2 September 1998, Week 1 August 1998, Week 5 August 1998, Week 4 August 1998, Week 3 August 1998, Week 2 August 1998, Week 1 July 1998, Week 5 July 1998, Week 4 July 1998, Week 3 July 1998, Week 2 July 1998, Week 1 June 1998, Week 5 June 1998, Week 4 June 1998, Week 3 June 1998, Week 2 June 1998, Week 1 May 1998, Week 5 May 1998, Week 4 May 1998, Week 3 May 1998, Week 2 May 1998, Week 1 April 1998, Week 5 April 1998, Week 4 April 1998, Week 3 April 1998, Week 2 April 1998, Week 1 March 1998, Week 5 March 1998, Week 4 March 1998, Week 3 March 1998, Week 2 March 1998, Week 1 February 1998, Week 5 February 1998, Week 4 February 1998, Week 3 February 1998, Week 2 February 1998, Week 1 January 1998, Week 5 January 1998, Week 4 January 1998, Week 3 January 1998, Week 2 January 1998, Week 1 December 1997, Week 5 December 1997, Week 4 December 1997, Week 3 December 1997, Week 2 December 1997, Week 1 November 1997, Week 5 November 1997, Week 4 November 1997, Week 3 November 1997, Week 2 November 1997, Week 1 October 1997, Week 5 October 1997, Week 4 October 1997, Week 3 October 1997, Week 2 October 1997, Week 1 September 1997, Week 5 September 1997, Week 4 September 1997, Week 3 September 1997, Week 2 September 1997, Week 1 August 1997, Week 5 August 1997, Week 4 August 1997, Week 3 August 1997, Week 2 August 1997, Week 1 July 1997, Week 5 July 1997, Week 4 July 1997, Week 3 July 1997, Week 2 July 1997, Week 1 June 1997, Week 5 June 1997, Week 4 June 1997, Week 3 June 1997, Week 2 June 1997, Week 1 May 1997, Week 5 May 1997, Week 4 May 1997, Week 3 May 1997, Week 2 May 1997, Week 1 April 1997, Week 5 April 1997, Week 4 April 1997, Week 3 April 1997, Week 2 April 1997, Week 1 March 1997, Week 5 March 1997, Week 4 March 1997, Week 3 March 1997, Week 2 March 1997, Week 1 February 1997, Week 5 February 1997, Week 4 February 1997, Week 3 February 1997, Week 2 February 1997, Week 1 January 1997, Week 5 January 1997, Week 4 January 1997, Week 3 January 1997, Week 2 January 1997, Week 1 December 1996, Week 5 December 1996, Week 4 December 1996, Week 3 December 1996, Week 2 December 1996, Week 1 November 1996, Week 5 November 1996, Week 4 November 1996, Week 3 November 1996, Week 2 November 1996, Week 1 October 1996, Week 5 October 1996, Week 4 October 1996, Week 3 October 1996, Week 2 October 1996, Week 1 September 1996, Week 5 September 1996, Week 4 September 1996, Week 3 September 1996, Week 2 September 1996, Week 1 August 1996, Week 5 August 1996, Week 4 August 1996, Week 3 August 1996, Week 2 August 1996, Week 1 July 1996, Week 5 July 1996, Week 4 July 1996, Week 3 July 1996, Week 2 July 1996, Week 1 June 1996, Week 5 June 1996, Week 4 June 1996, Week 3 June 1996, Week 2 June 1996, Week 1 May 1996, Week 5 May 1996, Week 4 May 1996, Week 3 May 1996, Week 2 May 1996, Week 1 April 1996, Week 5 April 1996, Week 4 April 1996, Week 3 April 1996, Week 2 April 1996, Week 1 March 1996, Week 5 March 1996, Week 4 March 1996, Week 3 March 1996, Week 2 March 1996, Week 1 February 1996, Week 5 February 1996, Week 4 February 1996, Week 3 February 1996, Week 2 February 1996, Week 1 January 1996, Week 5 January 1996, Week 4 January 1996, Week 3 January 1996, Week 2 January 1996, Week 1 December 1995, Week 5 December 1995, Week 4 December 1995, Week 3 December 1995, Week 2 December 1995, Week 1 November 1995, Week 5 November 1995, Week 4 November 1995, Week 3 November 1995, Week 2 November 1995, Week 1 October 1995, Week 5 October 1995, Week 4 October 1995, Week 3 October 1995, Week 2 October 1995, Week 1 September 1995, Week 5 September 1995, Week 4 September 1995, Week 3 September 1995, Week 2 September 1995, Week 1 August 1995, Week 5 August 1995, Week 4 August 1995, Week 3 August 1995, Week 2 August 1995, Week 1 July 1995, Week 5 July 1995, Week 4 July 1995, Week 3 July 1995, Week 2 July 1995, Week 1 June 1995, Week 5 June 1995, Week 4 June 1995, Week 3 June 1995, Week 2 June 1995, Week 1 May 1995, Week 5 May 1995, Week 4 May 1995, Week 3 May 1995, Week 2 May 1995, Week 1 April 1995, Week 5 April 1995, Week 4 April 1995, Week 3 April 1995, Week 2 April 1995, Week 1 March 1995, Week 5 March 1995, Week 4 March 1995, Week 3 March 1995, Week 2 March 1995, Week 1 February 1995, Week 4 February 1995, Week 3 February 1995, Week 2 February 1995, Week 1 January 1995, Week 5 January 1995, Week 4 January 1995, Week 3 January 1995, Week 2 January 1995, Week 1 December 1994, Week 5 December 1994, Week 4 December 1994, Week 3 December 1994, Week 2 December 1994, Week 1 November 1994, Week 5 November 1994, Week 4 November 1994, Week 3 November 1994, Week 2 November 1994, Week 1 October 1994, Week 5 October 1994, Week 4 October 1994, Week 3 October 1994, Week 2 October 1994, Week 1 September 1994, Week 5 September 1994, Week 4 September 1994, Week 3 September 1994, Week 2 September 1994, Week 1 August 1994, Week 5 August 1994, Week 4 August 1994, Week 3 August 1994, Week 2 August 1994, Week 1 July 1994, Week 5 July 1994, Week 4 July 1994, Week 3 July 1994, Week 2 July 1994, Week 1 June 1994, Week 5 June 1994, Week 4 June 1994, Week 3 June 1994, Week 2 June 1994, Week 1 May 1994, Week 5 May 1994, Week 4 May 1994, Week 3 May 1994, Week 2 May 1994, Week 1 April 1994, Week 5 April 1994, Week 4 April 1994, Week 3 April 1994, Week 2 April 1994, Week 1 March 1994, Week 5 March 1994, Week 4 March 1994, Week 3 March 1994, Week 2 March 1994, Week 1 February 1994, Week 4 February 1994, Week 3 February 1994, Week 2 February 1994, Week 1 February 1994 January 1994 December 1993 November 1993
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